Successful closure of ventricular septal defect in a patient with noncompaction of the left ventricular myocardium

Ömer Faruk Doğan, Metin Demircin

Department of Cardiovascular Surgery, Medical Faculty of Hacettepe University, Ankara

Left ventricular noncompaction (LVNC) is a rare clinical condition characterized by numerous prominent intertrabecular recesses in the ventricle, and is an unclassified cardiomyopathy. The pathology has been almost invariably associated with other congenital cardiac malformations. We presented a twoyear- old patient with LVNC accompanied by ventricular septal defect (VSD). Two-dimensional echocardiography showed a perimembranous VSD, 8 mm in size, and LVNC. The ratio of left ventricular noncompacted/compacted myocardial layers was 4.2. Since there was no evidence for cardiomyopathy, the patient underwent open heart surgery for the closure of VSD. Four months after the operation, echocardiographic findings showed normal myocardial performance.

Keywords : Ekokardiyografi; kardiyomiyopati; kalp defekti, doğuştan/komplikasyon/cerrahi; kalp septal defekti, ventriküler; kalp ventrikülü

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