ISSN : 1301-5680
e-ISSN : 2149-8156
TURKISH JOURNAL OF
THORACIC AND
CARDIOVASCULAR SURGERY
Turkish Journal of Thoracic and Cardiovascular Surgery     
Is isolated dextrocardia a feature of left-sided Poland's syndrome?
Nurettin Yiyit1, Turgut Isıtmangil1, Serkan Arıbal2
1Deparment of Thoracic Surgery, GMMA Haydarpaşa Training Hospital, İstanbul, Turkey
2Department of Radiology, Aksaz Military Hospital, Muğla, Turkey
DOI : 10.5606/tgkdc.dergisi.2015.10736
Background: In this study, we investigate the relationship between Poland’s syndrome and dextrocardia.

Methods: The diagnosis of Poland’s syndrome with dextrocardia was made in eight male patients (mean age 21 years; range 19 to 25 years) between January 2005 and December 2013. All patients had left-sided syndrome. The patients were evaluated in terms of additional anomalies.

Results: Isolated dextrocardia, the absence of the left pectoral muscle, and breast anomalies were detected in all patients. The absence or hypoplasia of the left serratus anterior muscle in three patients, partial rib agenesis in five patients, contralateral pectus carinatum deformity in three patients, scoliosis in one patient, brachysyndactyly in one patient, and palmar hyperhidrosis in one patient were identified. Three patients had Poland’s syndrome with dextrocardia without rib agenesis. Left-sided Sprengel’s deformity was observed in three patients.

Conclusion: Our case series may support the view that dextrocardia may be a feature of left-sided Poland’s syndrome and the combination of Poland’s syndrome and isolated dextrocardia may be present without rib agenesis.

Keywords : Dextrocardia; partial rib agenesis; Poland’s syndrome
Viewed : 4548
Downloaded : 1053