ISSN : 1301-5680
e-ISSN : 2149-8156
TURKISH JOURNAL OF
THORACIC AND
CARDIOVASCULAR SURGERY
Turkish Journal of Thoracic and Cardiovascular Surgery     
A giant pulmonary artery aneurysm associated with congenital keratoglobus
İhsan Alur1, Tevfik Güneş1, Gökhan Pekel2, Bilgin Emrecan1
1Departments of Cardiovascular Surgery, Medical Faculty of Pamukkale University, Denizli, Turkey
2Departments of Ophthalmology, Medical Faculty of Pamukkale University, Denizli, Turkey
Pulmonary artery aneurysms are rare pathologies which may present with Marfan syndrome, Ehler- Danlos syndrome, or collagen tissue diseases. These aneurysms may originate from non-congenital causes, such as pulmonary arterial hypertension, tuberculosis, syphilis, candida, mucormycosis, Behçet’s disease, giantcell arteritis, or post-trauma vasculitis. The presence of pulmonary artery aneurysm and those of the ascending aorta and aortic root along with a single coronary ostium abnormality accompanied by congenital keratoglobus is a very rare condition. Herein, we present a 33-year-old male with congenital keratoglobus who underwent surgery for a pulmonary artery aneurysm associated with aneurysms of the aorta and aortic root, as well as advanced aortic insufficiency.
Keywords : Aneurysm; aortic root aneurysm; congenital keratoglobus; pulmonary artery
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