ALCAPA syndrome in an asymptomatic young soccer player

Mehmet Gökhan Ramoğlu

doi:10.5606/tgkdc.dergisi.2019.16320

Mehmet Gökhan Ramoğlu¹, Mustafa Orhan Bulut², Serdar Epçaçan¹, Mehmet Dedemoğlu³

¹Department of Pediatric Cardiology, University of Health Sciences, Van Training and Research Hospital, Van, Turkey
²Department of Pediatric Cardiology, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Training and Research Hospital, İstanbul, Turkey
³Department of Pediatric Cardiovascular Surgery, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Training and Research Hospital, İstanbul, Turkey

DOI : 10.5606/tgkdc.dergisi.2019.16320

Anomalous origin of left coronary artery from pulmonary artery syndrome is a rare, but severe congenital cardiac malformation. It is an important cause of dilated cardiomyopathy and left heart failure during infancy and, if left untreated, the prognosis is poor with an overall mortality rate over 90%. About 15% of patients can survive beyond the first year of life, depending on the development of collateral circulation and may present with angina, dyspnea, syncope, and arrhythmias. Myocardial infarction and sudden cardiac death may be the only and the first symptom in some cases. The treatment of choice for this syndrome is urgent surgical intervention with favorable long-term outcomes. Herein, we present an asymptomatic adolescent active sportsman who was diagnosed with anomalous origin of left coronary artery from pulmonary artery syndrome and underwent a successful surgery.

Keywords : ALCAPA, asymptomatic, coronary anomaly, left heart failure

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