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10.5606/tgkdc.dergisi.2013.5574
Anatomically corrected malposition of the great arteries
Utku Arman Örün, Özben Ceylan, Selmin Karademir, Filiz Şenocak, Burhan Öcal
Dr. Sami Ulus Kadın Doğum, Çocuk Sağlığı ve Hastalıkları Eğitim ve Araştırma Hastanesi, Pediatrik Kardiyoloji Kliniği, Ankara, Türkiye
DOI : 10.5606/tgkdc.dergisi.2013.5574
Anatomically corrected malposition of the great arteries
(ACMGA) is characterized by atrioventricular concordance or
discordance and ventriculoarterial concordances with arterial
roots arising parallel to each other. Abnormally related
aorta arises from the left ventricle, while abnormally related
pulmonary artery arises from the right ventricle. In this article,
we report two male cases who were five-months-old and
two-years-old diagnosed with ACMGA. Echocardiographic
examination revealed atrial situs solitus (S), ventricular
d-loop (D) and l-malposition (L) of great arteries [Van
Praagh’s symbolic nomenclature (S.D.L)]. The diagnosis was
confirmed by cardiac catheterization and angiography. Both
patients were operated. During the operation, morphologic
findings of ACMGA were confirmed. In this article, we
emphasize that anatomically corrected malposition is a rare
condition and it can be confused with conditions such as
transposition of great arteries and congenitally corrected
transposition of great arteries, when it is not considered.
Keywords : Anatomically corrected malposition; atrioventricular concordance; atrioventricular discordance; cardiac catheterization
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