A rare cause of aortic valve stenosis: Ochronosis

Atakan Atalay

doi:10.5606/tgkdc.dergisi.2018.15552

Atakan Atalay¹, Vural Polat¹, Nesrin Turhan², İrfan Taşoğlu¹

¹Department of Cardiovascular Surgery, Türkiye Yüksek İhtisas Training and Research Hospital, Ankara, Turkey
²Department of Pathology, Türkiye Yüksek İhtisas Training and Research Hospital, Ankara, Turkey

DOI : 10.5606/tgkdc.dergisi.2018.15552

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Ochronosis is an autosomal recessive metabolic disorder which may cause aortic valve stenosis. In this article, we report a 58-yearold male patient with alkaptonuria who presented to our institute with severe aortic valve stenosis. He underwent successful aortic valve replacement with a mechanical prosthesis. The deposition of foreign material in valvular tissue is a rare case scenario which may result in serious problems, the management of which may necessitate valve replacement with prosthetic heart valves.

Keywords : Alkaptonuria; aortic valve; ochronosis

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