A prenatally diagnosed newborn with an intracardiac rhabdomyoma obstructing the left ventricular outflow tract

Mustafa Kır,

doi:10.5606/tgkdc.dergisi.2011.099

Mustafa Kır¹, Hüdai Çatalyürek², Ulaş Karadaş¹, Nurettin Ünal¹, Gül Sağın Saylam¹

¹Dokuz Eylül Üniversitesi Tıp Fakültesi, Çocuk Sağlığı ve Hastalıkları Anabilim Dalı, İzmir
²Dokuz Eylül Üniversitesi Tıp Fakültesi, Kalp ve Damar Cerrahisi Anabilim Dalı, İzmir

DOI : 10.5606/tgkdc.dergisi.2011.099

Primary tumors of the heart are rarely seen in childhood. Rhabdomyoma, which has a benign course and usually resolves spontaneously, constitutes the majority. However, rhabdomyomas which cause permanent rhythm problems, myocardial dysfunction, and ventricular inflow or outflow obstruction, should be removed surgically. In this article, we report the case of a newborn who was prenatally diagnosed with rhabdomyoma associated with severe left ventricular outflow obstruction. There were two small masses in the right ventricle as well. These masses were considered to be rhabdomyomas since they were multiple and appeared to be intracardiac with echocardiography. The left ventricular mass was removed through the aorta on the first postnatal day. The right ventricular masses were observed to regress during the clinical follow-up.

Keywords : Left ventricular outflow tract obstruction; prenatal diagnosis; rhabdomyoma

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