Patents with Ventricular Septal Defect (VSD) and
pulmonary atresia with major aortopulmonary
collateral arteries (MAPCAs) are not appopriate for
one stage repair, because they have hypoplastic
pulmonary arteries (PAs) and major arborization
defects in their lungs. Patient without hypoplastic
PAs and arborization defects are suitable for one
stage total correction. However if they have hypoplastic PAs, the approach should be a shunt operation at first stage before the total correction
procedure. Many authors have reported studies
about unifocalization as the first stage operation and
the correction by replacement of a conduit between
right ventricle and PAs as the second stage.
If direct anastomosis of MAPCAs with central PAs is
difficult technically, interposition grafts should be
used. In our 17 year old patient we have unifocalised
MAPCAs with left and right PA's using polytetraflouroethylene (PTFE) tube grafts through median
sternotomy. With this case, we want to report that
performing bilateral unifocalization operation
through median sternotomy is practicable.