Double-outlet right ventricle (DORV) is a very rare anomaly which can be presented with many cardiac abnormalities and ventricular septal defect (VSD) in particular. Clinical findings usually appear in the newborn period, which allows us to diagnose in the early period of life. The clinical findings vary according to the type of accompanying VSD and whether there are additional cardiac abnormalities such as pulmonary stenosis. These patients often present with cyanosis, congestive heart failure findings and pulmonary infections based on interstitial pulmonary edema. The treatment is surgical. Bronchiectasis is a serious pulmonary problem which may be encountered in some patients with frequent pulmonary infections. In this article, a 20-year-old male case with the simultaneous presence of bronchiectasis due to frequent pulmonary infections and DORV, VSD, pulmonary stenosis and atrial septal defect is presented. The risk factors of any pulmonary resection and cardiac surgery applied were also discussed.

Keywords : Atrial septal defect; bronchiectasis; double-outlet right ventricle; pulmoner stenosis; ventricular septal defect