A 29-year-old male patient with one year history of Behçet's disease was admitted to a nearby hospital with the complaints of abdominal and back pain. His medical history included familial Mediterranean fever (FMF) for 16 years. Thoracoabdominal computed tomography revealed a giant saccular aneurysmal dilatation of the abdominal aorta at the infrarenal level. He was referred to our institution. Endovascular stent-graft infection developed during follow-up after an endovascular stent-graft was placed. At fourth month of follow-up, the patient was urgently operated due to a rupture during endovascular drainage of a retroperitoneal abscess and an axillobifemoral bypass graft was implanted. This case demonstrates that endovascular stent-grafting should be a valid therapeutic alternative in the management of urgent treatment of abdominal aortic aneurysm in active Behçet's disease and AAA, as the surgical repair of active Behçet’s disease aneurysm is a very highly risky. However, this case also highlights that endovascular stent-grafting may be highly risky for patients with active Behçet’s disease, particularly who are on immunosuppressive drug regimen. Endovascular prosthesis infection following endovascular abdominal aneurysm repair is a dramatic event and its diagnosis and treatment are extremely complex and require a multidisciplinary approach.

Keywords : Abdominal aortic aneurysm; Behçet's disease; familial Mediterranean fever; graft infection