ISSN : 1301-5680
e-ISSN : 2149-8156
Turkish Journal of Thoracic and Cardiovascular Surgery     
Sympathetic denervation in the treatment of fatal arrhythmias in long QT syndrome with restrictive cardiomyopathy
Serhat Koca1, Feyza Ayşenur Paç1, Alkın Yazıcıoğlu2, Dursun Aras3, Erdal Yekeler2
1Departments of Pediatric Cardiology, Türkiye Yüksek İhtisas Training and Research Hospital, Ankara, Turkey
2Departments of Thoracic Surgery, Türkiye Yüksek İhtisas Training and Research Hospital, Ankara, Turkey
3Departments of Cardiology, Türkiye Yüksek İhtisas Training and Research Hospital, Ankara, Turkey
DOI : 10.5606/tgkdc.dergisi.2016.12405
A 12-year-old female patient was diagnosed with long QT syndrome during screening performed as another member of her family had long QT syndrome. Beta-blocker therapy was initiated and an intra-cardiac defibrillator was implanted for syncopes. During follow-up, as defibrillator shocks suggesting ventricular tachycardia were detected, ablation was performed for the polymorphic ventricular extrasystoles, which were considered to induce ventricular tachycardia. Despite this intervention and ongoing proper defibrillator shocking, restrictive cardiomyopathy signs were added to the clinical presentation. The patient underwent left cardiac sympathetic denervation by the videoassisted thoracoscopy. During a three-month postoperative follow-up, no intra-cardiac defibrillator shocking occurred. Video-assisted thoracoscopic left cardiac sympathetic denervation can be safely and effectively performed in long QT patients with life-threatening ventricular arrhythmias.
Keywords : Long QT syndrome; sympathectomy; thoracoscopy
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