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10.5606/tgkdc.dergisi.2016.12405
Sympathetic denervation in the treatment of fatal arrhythmias in long QT syndrome with restrictive cardiomyopathy
Serhat Koca1, Feyza Ayşenur Paç1, Alkın Yazıcıoğlu2, Dursun Aras3, Erdal Yekeler2
1Departments of Pediatric Cardiology, Türkiye Yüksek İhtisas Training and Research Hospital, Ankara, Turkey
2Departments of Thoracic Surgery, Türkiye Yüksek İhtisas Training and Research Hospital, Ankara, Turkey
3Departments of Cardiology, Türkiye Yüksek İhtisas Training and Research Hospital, Ankara, Turkey
DOI : 10.5606/tgkdc.dergisi.2016.12405
A 12-year-old female patient was diagnosed with long
QT syndrome during screening performed as another
member of her family had long QT syndrome. Beta-blocker
therapy was initiated and an intra-cardiac defibrillator was
implanted for syncopes. During follow-up, as defibrillator
shocks suggesting ventricular tachycardia were detected,
ablation was performed for the polymorphic ventricular
extrasystoles, which were considered to induce ventricular
tachycardia. Despite this intervention and ongoing proper
defibrillator shocking, restrictive cardiomyopathy signs
were added to the clinical presentation. The patient
underwent left cardiac sympathetic denervation by the videoassisted
thoracoscopy. During a three-month postoperative
follow-up, no intra-cardiac defibrillator shocking occurred.
Video-assisted thoracoscopic left cardiac sympathetic
denervation can be safely and effectively performed in long
QT patients with life-threatening ventricular arrhythmias.
Keywords : Long QT syndrome; sympathectomy; thoracoscopy
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