ISSN : 1301-5680
e-ISSN : 2149-8156
Turkish Journal of Thoracic and Cardiovascular Surgery     
A rare association of Poland’s syndrome and pneumothorax
Özgür İşgörücü, Yunus Aksoy, Necati Çıtak, Songül Büyükkale, Adnan Sayar
Yedikule Göğüs Hastalıkları ve Göğüs Cerrahisi Eğitim ve Araştırma Hastanesi, Göğüs Cerrahisi Kliniği, İstanbul, Türkiye
DOI : 10.5606/tgkdc.dergisi.2017.13727
Poland’s syndrome is a rare congenital anomaly, characterized by a partial or complete absence of pectoralis major muscle, absence of minor pectoral muscles, absence or hypoplasia of breasts and/or nipples, absence of ribs in a varying degree, hand abnormalities, and hypoplasia of the subcutaneous tissue. However, its coexistence with pneumothorax is very rare. A 51-year-old male patient was admitted to our emergency department with complaints of progressive chest pain and dyspnea which began a week ago. Physical examination revealed that breath sounds decreased on the right side with an absence of pectoralis major muscle. Plain chest X-ray showed total pneumothorax on the right side. The patient underwent bullectomy and pleural abrasion using video-assisted thoracoscopic surgery. We present this case to draw attention to the rare association of Poland’s syndrome with spontaneous pneumothorax.
Keywords : Congenital anomaly; Poland’s syndrome; pneumothorax; surgery
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