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10.5606/tgkdc.dergisi.2017.13727
A rare association of Polands syndrome and pneumothorax
Özgür İşgörücü, Yunus Aksoy, Necati Çıtak, Songül Büyükkale, Adnan Sayar
Yedikule Göğüs Hastalıkları ve Göğüs Cerrahisi Eğitim ve Araştırma Hastanesi, Göğüs Cerrahisi Kliniği, İstanbul, Türkiye
DOI : 10.5606/tgkdc.dergisi.2017.13727
Polands syndrome is a rare congenital anomaly,
characterized by a partial or complete absence of pectoralis
major muscle, absence of minor pectoral muscles, absence
or hypoplasia of breasts and/or nipples, absence of ribs
in a varying degree, hand abnormalities, and hypoplasia
of the subcutaneous tissue. However, its coexistence with
pneumothorax is very rare. A 51-year-old male patient was
admitted to our emergency department with complaints
of progressive chest pain and dyspnea which began a
week ago. Physical examination revealed that breath
sounds decreased on the right side with an absence of
pectoralis major muscle. Plain chest X-ray showed total
pneumothorax on the right side. The patient underwent
bullectomy and pleural abrasion using video-assisted
thoracoscopic surgery. We present this case to draw
attention to the rare association of Polands syndrome with
spontaneous pneumothorax.
Keywords : Congenital anomaly; Polands syndrome; pneumothorax; surgery
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