A rare association of Polands syndrome and pneumothorax

doi:10.5606/tgkdc.dergisi.2017.13727

A rare association of Polands syndrome and pneumothorax

Özgür İşgörücü, Yunus Aksoy, Necati Çıtak, Songül Büyükkale, Adnan Sayar

Yedikule Göğüs Hastalıkları ve Göğüs Cerrahisi Eğitim ve Araştırma Hastanesi, Göğüs Cerrahisi Kliniği, İstanbul, Türkiye

DOI : 10.5606/tgkdc.dergisi.2017.13727

Polands syndrome is a rare congenital anomaly, characterized by a partial or complete absence of pectoralis major muscle, absence of minor pectoral muscles, absence or hypoplasia of breasts and/or nipples, absence of ribs in a varying degree, hand abnormalities, and hypoplasia of the subcutaneous tissue. However, its coexistence with pneumothorax is very rare. A 51-year-old male patient was admitted to our emergency department with complaints of progressive chest pain and dyspnea which began a week ago. Physical examination revealed that breath sounds decreased on the right side with an absence of pectoralis major muscle. Plain chest X-ray showed total pneumothorax on the right side. The patient underwent bullectomy and pleural abrasion using video-assisted thoracoscopic surgery. We present this case to draw attention to the rare association of Polands syndrome with spontaneous pneumothorax.

Keywords : Congenital anomaly; Polands syndrome; pneumothorax; surgery

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