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10.5606/tgkdc.dergisi.2019.16320
ALCAPA syndrome in an asymptomatic young soccer player
Mehmet Gökhan Ramoğlu1, Mustafa Orhan Bulut2, Serdar Epçaçan1, Mehmet Dedemoğlu3
1Department of Pediatric Cardiology, University of Health Sciences, Van Training and Research Hospital, Van, Turkey
2Department of Pediatric Cardiology, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Training and Research Hospital, İstanbul, Turkey
3Department of Pediatric Cardiovascular Surgery, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Training and Research Hospital, İstanbul, Turkey
DOI : 10.5606/tgkdc.dergisi.2019.16320
Anomalous origin of left coronary artery from pulmonary artery
syndrome is a rare, but severe congenital cardiac malformation.
It is an important cause of dilated cardiomyopathy and left
heart failure during infancy and, if left untreated, the prognosis
is poor with an overall mortality rate over 90%. About 15% of
patients can survive beyond the first year of life, depending on
the development of collateral circulation and may present with
angina, dyspnea, syncope, and arrhythmias. Myocardial infarction
and sudden cardiac death may be the only and the first symptom
in some cases. The treatment of choice for this syndrome is urgent
surgical intervention with favorable long-term outcomes. Herein,
we present an asymptomatic adolescent active sportsman who
was diagnosed with anomalous origin of left coronary artery from
pulmonary artery syndrome and underwent a successful surgery.
Keywords : ALCAPA, asymptomatic, coronary anomaly, left heart failure
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