A rare association of left pulmonary artery sling with Scimitar syndrome: Recurrent wheezing and respiratory distress in a pediatric patient

Emine Azak

doi:10.5606/tgkdc.dergisi.2021.20227

Emine Azak¹, İbrahim İlker Çetin², Tevfik Karagöz³, Metin Demircin⁴

¹Department of Pediatric Cardiology, University of Health Sciences, Ankara City Hospital, Ankara, Turkey
²Department of Pediatric Cardiology, Yıldırım Beyazıt University Faculty of Medicine, Ankara, Turkey
³Department of Pediatric Cardiology, Hacettepe University Faculty of Medicine, Ankara, Turkey
⁴Department of Cardiovascular Surgery, Hacettepe University Faculty of Medicine, Ankara, Turkey

DOI : 10.5606/tgkdc.dergisi.2021.20227

Congenital anomalies of the heart and great vessels may lead to localized recurrent pulmonary infections through different mechanisms. Pulmonary artery sling (left pulmonary artery originating from the right pulmonary artery) and Scimitar syndrome are rare causes of wheezing in infants. An 18-month-old female infant with left pulmonary artery sling, Scimitar syndrome, and an anomalous connection of left pulmonary veins to the left atrium was admitted to our clinic. She successfully underwent transcatheter embolization using the Vascular Plug-II on the anomalous systemic arterial supply and repair of pulmonary arterial sling and Scimitar anomaly via a median sternotomy. In conclusion, diagnosis of left pulmonary arterial sling accompanied by abnormalities can be missed in some cases using echocardiography. It may be necessary to conduct more advanced imaging methods before deciding the treatment method to be performed in these patients.

Keywords : Anomalous pulmonary veins, computed tomography angiography, pulmonary artery sling, Scimitar syndrome, vascular plug-II

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