Management of a primary cardiac leiomyosarcoma in a young woman

Mehmet Akif Önalan

doi:10.5606/tgkdc.dergisi.2021.21040

Mehmet Akif Önalan¹, Ahmet Demirkaya², Kemal Behzatoglu³, Ersin Erek¹

¹Department of Cardiovascular Surgery, Acıbadem Mehmet Ali Aydınlar University Faculty of Medicine, Istanbul, Turkey
²Department of Thoracic Surgery, Acıbadem Mehmet Ali Aydınlar University Faculty of Medicine, Istanbul, Turkey
³Department of Pathology, Acıbadem Mehmet Ali Aydınlar University Faculty of Medicine, Istanbul, Turkey

DOI : 10.5606/tgkdc.dergisi.2021.21040

Cardiac leiomyosarcoma is an extremely rare tumor with a poor prognosis. An 18-year-old female patient was admitted to our clinic with a left atrial leiomyosarcoma extending to the right lower pulmonary veins. We performed complete tumor excision by the right anterolateral mini-thoracotomy approach using minimally invasive techniques. After pathological confirmation of the tumor, right lower lobectomy was performed with the same incision one week later to prevent recurrence. Although no tumor remnant was found in the lobectomy specimen, adjuvant chemotherapy was started. No recurrence was detected during the 12-month follow-up. In conclusion, the right submammarian minithoracotomy approach has the advantages of its less invasive nature and suitability for complete tumor resection with lobectomy.

Keywords : Cardiac neoplasm, leiomyosarcoma, surgery

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