RENDU OSLER WEBER DISEASE ASSOCIATED WITH SYSTEMIC SUPPLY TO PULMONARY ARTERIOVENOUS FISTULA

Alpay Sarper, *Necdet Öz, Abid Demircan, **Erol Işın

Akdeniz Üniversitesi Tıp Fakültesi, Göğüs Cerrahisi Ana Bilim Dalı, Antalya
*SSK Antalya Hastanesi, Göğüs Cerrahisi Kliniği, Antalya
**Antalya Göğüs Cerrahisi Merkezi, Göğüs Cerrahisi Kliniği, Antalya

A 20-year-old man presented with hemoptysis, epistaxis and severe fatique. Chest X-ray film revealed an abnormal shadow. On the physical examination, multiple telangiectases were found at the oral and nasal mucous membrane and tongue. Computed tomography and pulmonary angiography showed an arteriovenous fistula of the left lower lobe. The diagnosis was Rendu Osler Weber Disease. Lobectomy was performed because of the systemic supply to the large pulmonary arteriovenous aneurysm.

Keywords : Rendu Osler Weber disease, pulmonary aneurysm, hereditary hemorrhagic telangiectasia, arteriovenous fitula

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