ISSN : 1301-5680
e-ISSN : 2149-8156
Turkish Journal of Thoracic and Cardiovascular Surgery     
Ebstein's anomaly in a 16-year-old child presenting with cyanosis and syncope
İbrahim Gökşin1, Ahmet Baltalarlı1, Harun Evrengül1, Mustafa Saçar2, Vefa Özcan1, Ercan Gürses3
1Pamukkale Üniversitesi Tıp Fakültesi, Kalp ve Damar Cerrahisi Anabilim Dalı, Denizli
2Pamukkale Üniversitesi Tıp Fakültesi, Kardiyoloji Anabilim Dalı, Denizli
3Pamukkale Üniversitesi Tıp Fakültesi, Kalp ve Damar Cerrahisi Anabilim Dalı, Anestezi ve Reanimasyon Anabilim Dalı, Denizli
Ebstein's anomaly is an uncommon malformation of the tricuspid valve, accounting for 0.5% of all congenital heart diseases. We presented a 16-year-old male child with type B Ebstein's anomaly, who presented with complaints of cyanosis and syncope. He was successfully operated on with the Carpentier's repair technique. Cyanosis completely disappeared just after the operation and the patient had an uneventful recovery period.
Keywords : Adolescent; cyanosis; Ebstein anomaly / complications / surgery ; syncope.
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