Current therapies for extra-abdominal fibromatosis of the chest wall: a silent giant mass

Alper Fındıkcıoğlu,

Alper Fındıkcıoğlu¹, Dalokay Kılıç², Emrah Koçer³, Bülent Celasun³, Ahmet Hatipoğlu²

¹Department of Thoracic Surgery, Başkent University Adana Training and Research Center, Adana
²Department of Thoracic Surgery, Medicine Faculty of Başkant University, Ankara
³Department of Pathology, Medicine Faculty of Başkant University, Ankara

Extra-abdominal fibromatosis (desmoid tumor) is a rare and benign lesion of soft tissue which has a strong tendency for local invasion and recurrence. We present a case of a 44-year-old woman with an asymptomatic, intrathoracic but extrapulmonary giant mass requiring wide surgical resection and reconstruction of the chest wall. The tumor which was greater than 10 cm in diameter, was found incidentally on a routine chest radiograph. The patient underwent wide chest wall resection and reconstruction with a sandwich graft. No recurrence has been observed during two years follow-up. Treatment modalities for recurrent and inoperable desmoid tumor include radiotherapy and estrogen antagonists, however, surgical resection with safety margins as for a malignant tumor is the primary treatment choice.

Keywords : Chest wall tumor; desmoid tumor; extra-abdominal fibromatosis

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