ISSN : 1301-5680
e-ISSN : 2149-8156
Turkish Journal of Thoracic and Cardiovascular Surgery     
An absent right superior vena cava with a persistent left superior vena cava combined with the presence of a ventricular septal defect in a pediatric patient: Implications for surgical correction
Orhan Saim Demirtürk1, Ayten Gümüş2, Mediha Hacer Ülger3, Murat Güvener1
1Department of Cardiovascular Surgery, Başkent University Adana Teaching and Research Center, Adana, Turkey
2Department of Pediatric Cardiology, Başkent University Adana Teaching and Research Center, Adana, Turkey
3Department of Anaesthesiology and Reanimation, Başkent University Adana Teaching and Research Center, Adana, Turkey
DOI : 10.5606/tgkdc.dergisi.2012.125
A persistent left superior vena cava in conjunction with a absent right superior vena cava is a very rare anomaly of venous circulation. In this article, we present a fouryear- old girl with a persistent left superior vena cava opening into a dilated coronary sinus and an absent right superior vena cava accompanied by a perimembraneous outlet ventricular septal defect which were corrected using cardiopulmonary bypass surgery.
Keywords : Absent right superior vena cava; persistent left superior vena cava; ventricular septal defect
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