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10.5606/tgkdc.dergisi.2016.12090
Univentricular heart and Cantrell syndrome in a pediatric case
Selim Aydın1, Dilek Suzan1, Muazzez Çevik2, Ender Ödemiş3, Ersin Erek1
1Acıbadem Üniversitesi Atakent Hastanesi, Kalp ve Damar Cerrahisi Bölümü, İstanbul, Türkiye
2Acıbadem Üniversitesi Atakent Hastanesi, Çocuk Cerrahisi Bölümü, İstanbul, Türkiye
3Acıbadem Üniversitesi Atakent Hastanesi, Çocuk Kardiyolojisi Bölümü, İstanbul, Türkiye
DOI : 10.5606/tgkdc.dergisi.2016.12090
Cantrell syndrome is a rare syndrome associated with varying
degrees of midline wall defects and congenital cardiac
anomalies. In this article, we report a six-year-old girl with
Cantrell syndrome associated with single ventricle, pulmonary
stenosis, ventricular diverticulum, bilateral superior vena
cava, lower sternal, and supra-umbilical abdominal anterior
wall defect. The patient, who had no previous intervention
despite severe cyanosis (SpO2: 65 to 70%) due to the parent
decision, underwent operation. Bilateral Glenn procedure,
resection of the ventricular diverticulum, and anterior
abdominal wall repair were performed in collaboration with
pediatric surgery. The patient was discharged uneventfully
with a SpO2 of 80 to 85%. No problem was observed in the
postoperative sixth month visit.
Keywords : Cantrell syndrome; single ventricle; ventricular diverticulum
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