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10.5606/tgkdc.dergisi.2018.16106
A case of mixed drainage total anomalous pulmonary venous return in an adult patient
Murat Meriç1, Serkan Yüksel1
1Department of Cardiology, Medicine Faculty of Ondokuz Mayıs University, Samsun, Turkey
DOI : 10.5606/tgkdc.dergisi.2018.16106
Total anomalous pulmonary venous return is observed in 1.5 to
3% of congenital heart diseases. Urgent surgical intervention is
required following the diagnosis, since severe heart failure is
accompanied by cyanosis from the first days of life in most of
the patients. This rare congenital heart disease is often managed
in adulthood with surgery. Patients who survive until adulthood
without a surgical intervention have a large atrial septal defect.
A 36-year-old female patient was admitted with complaints
of fatigability, shortness of breath, and cyanosis of the lips.
Total anomalous pulmonary venous return, secundum-type
atrial septal defect, ventricular septal defect, and pulmonary
hypertension were diagnosed by transthoracic echocardiography
and catheter angiography. After medical treatment, surgery
was planned for the patient who responded to the pulmonary
vasoreactivity test with iloprost.
Keywords : Adult congenital heart disease; atrial septal defect; pulmonary hypertension; total anomalous pulmonary venous return; ventricular septal defect
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