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10.5606/tgkdc.dergisi.2024.25705
Congenital diaphragmatic hernia
Elçin Ersöz Köse1, İrfan Yalçınkaya1
1Department of Thoracic Surgery, Health Sciences University Istanbul Hamidiye Medical Faculty, Süreyyapaşa Chest Diseases and Thoracic Surgery Hospital, Istanbul, Türkiye
DOI : 10.5606/tgkdc.dergisi.2024.25705
Congenital diaphragmatic hernia (CDH) is a rare developmental
defect of the diaphragm, characterized by the herniation
of abdominal contents into the chest, resulting in varying
degrees of pulmonary hypoplasia and pulmonary hypertension.
Significant advances in the prenatal diagnosis and identification
of prognostic factors have resulted in the continued refinement of
the approach to fetal therapies for CDH. In the postnatal period,
protocolized approaches to lung-protective ventilation, nutrition,
prevention of infection, and early aggressive management of
pulmonary hypertension have led to improved outcomes in
infants with CDH. Surgical repair of CDH is not urgent in most
circumstances and can be delayed until the pulmonary status of
the patient has stabilized. This article provides a comprehensive
review of CDH, focusing on the complex pathophysiology,
advances in prenatal diagnosis, fetal interventions, and optimal
postnatal management of CDH.
Keywords : Bochdalek hernia, diaphragm, Morgagni hernia, pediatric, surgery
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