Univentricular heart and Cantrell syndrome in a pediatric case

Selim Aydın,

doi:10.5606/tgkdc.dergisi.2016.12090

Selim Aydın¹, Dilek Suzan¹, Muazzez Çevik², Ender Ödemiş³, Ersin Erek¹

¹Acıbadem Üniversitesi Atakent Hastanesi, Kalp ve Damar Cerrahisi Bölümü, İstanbul, Türkiye
²Acıbadem Üniversitesi Atakent Hastanesi, Çocuk Cerrahisi Bölümü, İstanbul, Türkiye
³Acıbadem Üniversitesi Atakent Hastanesi, Çocuk Kardiyolojisi Bölümü, İstanbul, Türkiye

DOI : 10.5606/tgkdc.dergisi.2016.12090

Cantrell syndrome is a rare syndrome associated with varying degrees of midline wall defects and congenital cardiac anomalies. In this article, we report a six-year-old girl with Cantrell syndrome associated with single ventricle, pulmonary stenosis, ventricular diverticulum, bilateral superior vena cava, lower sternal, and supra-umbilical abdominal anterior wall defect. The patient, who had no previous intervention despite severe cyanosis (SpO2: 65 to 70%) due to the parent decision, underwent operation. Bilateral Glenn procedure, resection of the ventricular diverticulum, and anterior abdominal wall repair were performed in collaboration with pediatric surgery. The patient was discharged uneventfully with a SpO2 of 80 to 85%. No problem was observed in the postoperative sixth month visit.

Keywords : Cantrell syndrome; single ventricle; ventricular diverticulum

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